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An autosomal recessive form of amelogenesis imperfecta, a defect of enamel formation. AI3C is characterized by generalized enamel hypocalcification affecting primary and secondary dentition. The surface of the enamel is rough and often stained. After eruption, the occlusal enamel on the molars disappears due to attrition, leaving a ring of intact enamel remaining on the sides.




Amelogenesis imperfecta, hypocalcification type, autosomal recessive
Amelogenesis imperfecta, type IIIC


Amelogenesis imperfecta


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