##gff-version 3 Q9XT75 UniProtKB Transit peptide 1 44 . . . Note=Mitochondrion;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9XT75 UniProtKB Chain 45 582 . . . ID=PRO_0000001222;Note=5-aminolevulinate synthase%2C erythroid-specific%2C mitochondrial Q9XT75 UniProtKB Active site 386 386 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q9XT75 UniProtKB Binding site 158 158 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q9XT75 UniProtKB Binding site 253 253 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q9XT75 UniProtKB Binding site 254 254 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q9XT75 UniProtKB Binding site 275 275 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q9XT75 UniProtKB Binding site 294 294 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q9XT75 UniProtKB Binding site 327 327 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q9XT75 UniProtKB Binding site 355 355 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q9XT75 UniProtKB Binding site 383 383 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q9XT75 UniProtKB Binding site 415 415 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q9XT75 UniProtKB Binding site 416 416 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q9XT75 UniProtKB Binding site 503 503 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q9XT75 UniProtKB Modified residue 386 386 . . . Note=N6-(pyridoxal phosphate)lysine;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557