##gff-version 3 Q9DC29 UniProtKB Chain 1 842 . . . ID=PRO_0000268678;Note=ATP-binding cassette sub-family B member 6 Q9DC29 UniProtKB Topological domain 1 26 . . . Note=Lumenal;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Transmembrane 27 47 . . . Note=Helical;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9DC29 UniProtKB Topological domain 48 72 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 Q9DC29 UniProtKB Transmembrane 73 93 . . . Note=Helical;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9DC29 UniProtKB Topological domain 94 106 . . . Note=Lumenal;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Transmembrane 107 127 . . . Note=Helical;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9DC29 UniProtKB Topological domain 128 147 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 Q9DC29 UniProtKB Transmembrane 148 168 . . . Note=Helical;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9DC29 UniProtKB Topological domain 169 185 . . . Note=Lumenal;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Transmembrane 186 206 . . . Note=Helical;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9DC29 UniProtKB Topological domain 207 263 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 Q9DC29 UniProtKB Transmembrane 264 284 . . . Note=Helical;Ontology_term=ECO:0000255,ECO:0000255;evidence=ECO:0000255,ECO:0000255|PROSITE-ProRule:PRU00441 Q9DC29 UniProtKB Topological domain 285 291 . . . Note=Lumenal;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Transmembrane 292 312 . . . Note=Helical;Ontology_term=ECO:0000255,ECO:0000255;evidence=ECO:0000255,ECO:0000255|PROSITE-ProRule:PRU00441 Q9DC29 UniProtKB Topological domain 313 375 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 Q9DC29 UniProtKB Transmembrane 376 396 . . . Note=Helical;Ontology_term=ECO:0000255,ECO:0000255;evidence=ECO:0000255,ECO:0000255|PROSITE-ProRule:PRU00441 Q9DC29 UniProtKB Topological domain 397 397 . . . Note=Lumenal;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Transmembrane 398 418 . . . Note=Helical;Ontology_term=ECO:0000255,ECO:0000255;evidence=ECO:0000255,ECO:0000255|PROSITE-ProRule:PRU00441 Q9DC29 UniProtKB Topological domain 419 499 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 Q9DC29 UniProtKB Transmembrane 500 520 . . . Note=Helical;Ontology_term=ECO:0000255,ECO:0000255;evidence=ECO:0000255,ECO:0000255|PROSITE-ProRule:PRU00441 Q9DC29 UniProtKB Topological domain 521 529 . . . Note=Lumenal;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Transmembrane 530 550 . . . Note=Helical;Ontology_term=ECO:0000255,ECO:0000255;evidence=ECO:0000255,ECO:0000255|PROSITE-ProRule:PRU00441 Q9DC29 UniProtKB Topological domain 551 842 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 Q9DC29 UniProtKB Domain 265 556 . . . Note=ABC transmembrane type-1;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00441 Q9DC29 UniProtKB Domain 590 824 . . . Note=ABC transporter;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00434 Q9DC29 UniProtKB Region 1 236 . . . Note=Required for ATPase activity;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Region 1 205 . . . Note=Required for the lysosomal targeting;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Binding site 599 599 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250 Q9DC29 UniProtKB Binding site 623 634 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00434 Q9DC29 UniProtKB Disulfide bond 8 26 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:Q9NP58 Q9DC29 UniProtKB Mutagenesis 170 170 . . . Note=Results in retention of the protein in the Golgi apparatus. S->G;Ontology_term=ECO:0000269;evidence=ECO:0000269|PubMed:23519333;Dbxref=PMID:23519333 Q9DC29 UniProtKB Mutagenesis 356 356 . . . Note=Results in retention of the protein in the Golgi apparatus. L->P;Ontology_term=ECO:0000269;evidence=ECO:0000269|PubMed:23519333;Dbxref=PMID:23519333 Q9DC29 UniProtKB Mutagenesis 579 579 . . . Note=Results in retention of the protein in the Golgi apparatus. G->E;Ontology_term=ECO:0000269;evidence=ECO:0000269|PubMed:23519333;Dbxref=PMID:23519333