##gff-version 3 Q9BSE5 UniProtKB Transit peptide 1 35 . . . Note=Mitochondrion;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9BSE5 UniProtKB Chain 36 352 . . . ID=PRO_0000002089;Note=Guanidino acid hydrolase%2C mitochondrial Q9BSE5 UniProtKB Region 11 49 . . . Note=Disordered;Ontology_term=ECO:0000256;evidence=ECO:0000256|SAM:MobiDB-lite Q9BSE5 UniProtKB Binding site 162 162 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00742 Q9BSE5 UniProtKB Binding site 185 185 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00742 Q9BSE5 UniProtKB Binding site 185 185 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00742 Q9BSE5 UniProtKB Binding site 187 187 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00742 Q9BSE5 UniProtKB Binding site 189 189 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00742 Q9BSE5 UniProtKB Binding site 276 276 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00742 Q9BSE5 UniProtKB Binding site 276 276 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00742 Q9BSE5 UniProtKB Binding site 278 278 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00742 Q9BSE5 UniProtKB Modified residue 193 193 . . . Note=N6-acetyllysine;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:A2AS89 Q9BSE5 UniProtKB Modified residue 217 217 . . . Note=N6-acetyllysine%3B alternate;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:A2AS89 Q9BSE5 UniProtKB Modified residue 217 217 . . . Note=N6-succinyllysine%3B alternate;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:A2AS89 Q9BSE5 UniProtKB Natural variant 105 105 . . . ID=VAR_023485;Note=Increased guanidino hydrolase activity toward taurocyamine%3B can hydrolyze guanidinopropanoate with low efficiency%3B inactive toward L-arginine. G->R;Ontology_term=ECO:0000269,ECO:0000269,ECO:0000269,ECO:0000269;evidence=ECO:0000269|PubMed:11804860,ECO:0000269|PubMed:14702039,ECO:0000269|PubMed:15489334,ECO:0000269|PubMed:36543883;Dbxref=dbSNP:rs6429757,PMID:11804860,PMID:14702039,PMID:15489334,PMID:36543883 Q9BSE5 UniProtKB Natural variant 140 140 . . . ID=VAR_048332;Note=R->Q;Ontology_term=ECO:0000269;evidence=ECO:0000269|PubMed:11804860;Dbxref=dbSNP:rs11580170,PMID:11804860 Q9BSE5 UniProtKB Sequence conflict 145 145 . . . Note=Y->C;Ontology_term=ECO:0000305;evidence=ECO:0000305