Q91293CPSM_AQUCTCarbamoyl-phosphate synthase [ammonia], mitochondrial6.3.4.16Carbamoyl-phosphate synthetase ICPSase IAquarana catesbeianaAmerican bullfrogRana catesbeianaEukaryotaMetazoaChordataCraniataVertebrataEuteleostomiAmphibiaBatrachiaAnuraNeobatrachiaRanoideaRanidaeRanaAquarana3,5,3'-Triiodothyronine-induced carbamyl-phosphate synthetase gene expression is stabilized in the liver of Rana catesbeiana tadpoles during heat shock.NUCLEOTIDE SEQUENCE [MRNA]Involved in the urea cycle of ureotelic animals where the enzyme plays an important role in removing excess ammonia from the cell.2 ATP + hydrogencarbonate + NH4(+) = 2 ADP + carbamoyl phosphate + 2 H(+) + phosphateRequires N-acetyl-L-glutamate (NAG) as an allosteric activator.MitochondrionAllosteric enzymeATP-bindingLigaseMitochondrionNucleotide-bindingRepeatTransit peptideUrea cycleN-acetyl-L-glutamateallosteric activatorN-acetyl-L-glutamateallosteric activatorN-acetyl-L-glutamateallosteric activatorN-acetyl-L-glutamateallosteric activatorN-acetyl-L-glutamateallosteric activatorN-acetyl-L-glutamateallosteric activatorMTRILSVFKTAKTGVLNAAAHRYRGFSKAGVRLMSVKAQTANLVLEDGTKIKGYSFGHPASVAGEVIFNTGLGGYVEAVTDPSYHGQILTLTNPIIGNGGAPDTKARDAYGLMKYIESENIQASGLLVLDYSHEYSHWGAVKSLSEWLHEEKVPALCGIDTRMLAKKIRDNKGAVLGKIEFEGQPVEFIDPNKRNLIAEVSTKETKVFGKGNPVRIVAVDCGVKHNIIRQLVKRGAEVHLVPWNHDFSQMEYDGLLITSGPGNPELAKPLIQNLKKVFQSDRPEPIFGICKGNEIAALAAGGKTYRLPMANRGQNQPVMITLNGQAFITAQNHAYAVDNNSLPAGWKPLFVNINDQSNEGIMHETKPIFTSQFHPEANPGPVDTEFLFDVYMSLIKKGKGTTLTSVMPKPALQSKRIDVAKVLILGSGGLSIGQAGEFDYSGSQAVKAMKEENVKTVLMNPNIASVQTNEVGLKQADTVYFLPITPQFVTEVIKAEKTDGIILGMGGQTALNCGVELFKRGVLKEYGVRVLGTSVESIMFTEDRQLFSDKLNEIKEPIAPSFAVESVKDALEAADKIGYPVMIRSAYALGGLGSGLCPDKETLTDLATKALAMTNQILVERSVVGWKEIEYEVVRDAADNCVTVCNMENVDAMGVHTGDSIVVAPCQTLSNEECQMLRAVSIKVVRHLGIVGECNIQFALHPTSLEYVIIEVNARLSRSSALASKATGYPLAFIAAKIALGIPLPEIKNVVSGKTTACFEPSLDYMVTKIPRWDLDRFHGASGLIGSSMKSVGEVMAIGRTFEESFQKALRMCHPSVDGFTSNLPMNKAWSSDVNLRKEMAEPTSTRMYSMAKAIQSGISLDEINKLTAIDKWFLYKMQGILNMEKTLKGSRSESVPEETLRRAKQIGFSDRYIGKCLGLSETQTRELRLNKNVKPWVKQIDTLAAEYPAITNYLYLTYNGQEHDIKFDDHGMMVLGCGPYHIGSSVEFDWCAVSSIRTLRHVGKKTVVVNCNPETVSTDFDECDKLYFEELSQERIMDVFQLEQCDGCIISVGGQIPNNLAVPLYKNGVKIMGTSPMQIDRAEDRSIFSAVLDELQIAQAPWKAVNSLDDALQFTKTVGYPCLLRPSYVLSGSAMNVVYGEEELKTFLAEATRVSQEHPVVITKFIEGAREVEMDAVGKEGRVISHAISEHVEDAGVHSGDATLMIPTQSISQGAIEKVKIATKKIATAFAISGPFNVQFLVRGNDVLVIECNLRASRSFPFVSKTLGVDFIDVATKVMIGEKIDESSLPTLERPVIPADYVGIKAPMFSWPRLRGADPVLKCEMASTGEVACFGQNVYSAFLKAMISTGFKLPQKGILIGIQHSFRPHFLGTAQTLKDEGFKLYATEATADWLNANDITATPVAWPSQEGQSGPSSIYKLIKEGNIDMVINLPNNNTKYVRDNFAIRRTAVDTGTALLTNFQVVKMFAEAIKYSGDLDAKSLFHYRQFGGAKPS
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