##gff-version 3 Q5R557 UniProtKB Transit peptide 1 49 . . . Note=Mitochondrion;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q5R557 UniProtKB Chain 50 587 . . . ID=PRO_0000290199;Note=5-aminolevulinate synthase%2C erythroid-specific%2C mitochondrial Q5R557 UniProtKB Active site 391 391 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q5R557 UniProtKB Binding site 163 163 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q5R557 UniProtKB Binding site 258 258 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q5R557 UniProtKB Binding site 259 259 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q5R557 UniProtKB Binding site 280 280 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q5R557 UniProtKB Binding site 299 299 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q5R557 UniProtKB Binding site 332 332 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q5R557 UniProtKB Binding site 360 360 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q5R557 UniProtKB Binding site 388 388 . . . Note=In other chain;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q5R557 UniProtKB Binding site 420 420 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q5R557 UniProtKB Binding site 421 421 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P22557 Q5R557 UniProtKB Binding site 508 508 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P18079 Q5R557 UniProtKB Modified residue 391 391 . . . Note=N6-(pyridoxal phosphate)lysine;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P08680