##gff-version 3 O08852 UniProtKB Signal peptide 1 23 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Chain 24 4293 . . . ID=PRO_0000354054;Note=Polycystin-1 O08852 UniProtKB Topological domain 24 3066 . . . Note=Extracellular;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3067 3087 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3088 3269 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3270 3290 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3291 3315 . . . Note=Extracellular;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3316 3336 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3337 3549 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3550 3570 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3571 3572 . . . Note=Extracellular;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3573 3593 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3594 3655 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3656 3676 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3677 3891 . . . Note=Extracellular;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3892 3912 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3913 3925 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3926 3946 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3947 3974 . . . Note=Extracellular;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 3975 3995 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 3996 4017 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 4018 4038 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 4039 4080 . . . Note=Extracellular;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Transmembrane 4081 4100 . . . Note=Helical;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Topological domain 4101 4293 . . . Note=Cytoplasmic;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Domain 24 67 . . . Note=LRRNT O08852 UniProtKB Repeat 68 91 . . . Note=LRR 1 O08852 UniProtKB Repeat 92 113 . . . Note=LRR 2 O08852 UniProtKB Domain 125 178 . . . Note=LRRCT O08852 UniProtKB Domain 177 271 . . . Note=WSC;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00558 O08852 UniProtKB Domain 272 359 . . . Note=PKD 1;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 415 530 . . . Note=C-type lectin;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00040 O08852 UniProtKB Domain 633 666 . . . Note=LDL-receptor class A%3B atypical O08852 UniProtKB Domain 849 922 . . . Note=PKD 2;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 929 1014 . . . Note=PKD 3;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1017 1123 . . . Note=PKD 4;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1121 1209 . . . Note=PKD 5;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1207 1292 . . . Note=PKD 6;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1288 1377 . . . Note=PKD 7;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1376 1463 . . . Note=PKD 8;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1462 1545 . . . Note=PKD 9;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1544 1629 . . . Note=PKD 10;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1630 1718 . . . Note=PKD 11;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1716 1802 . . . Note=PKD 12;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1804 1886 . . . Note=PKD 13;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1885 1970 . . . Note=PKD 14;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 1972 2053 . . . Note=PKD 15;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 2056 2144 . . . Note=PKD 16;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00151 O08852 UniProtKB Domain 2142 2828 . . . Note=REJ;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00511 O08852 UniProtKB Domain 3004 3053 . . . Note=GPS;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00098 O08852 UniProtKB Domain 3110 3225 . . . Note=PLAT;Ontology_term=ECO:0000255;evidence=ECO:0000255|PROSITE-ProRule:PRU00152 O08852 UniProtKB Region 613 632 . . . Note=Disordered;Ontology_term=ECO:0000256;evidence=ECO:0000256|SAM:MobiDB-lite O08852 UniProtKB Region 4150 4197 . . . Note=Disordered;Ontology_term=ECO:0000256;evidence=ECO:0000256|SAM:MobiDB-lite O08852 UniProtKB Region 4235 4293 . . . Note=Disordered;Ontology_term=ECO:0000256;evidence=ECO:0000256|SAM:MobiDB-lite O08852 UniProtKB Coiled coil 4210 4241 . . . Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Compositional bias 4154 4197 . . . Note=Polar residues;Ontology_term=ECO:0000256;evidence=ECO:0000256|SAM:MobiDB-lite O08852 UniProtKB Compositional bias 4261 4293 . . . Note=Polar residues;Ontology_term=ECO:0000256;evidence=ECO:0000256|SAM:MobiDB-lite O08852 UniProtKB Site 3040 3041 . . . Note=Cleavage%3B by autolysis;Ontology_term=ECO:0000250;evidence=ECO:0000250 O08852 UniProtKB Modified residue 4156 4156 . . . Note=Phosphoserine%3B by PRKX%3B in vitro;Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P98161 O08852 UniProtKB Glycosylation 50 50 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 89 89 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 116 116 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 121 121 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 187 187 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 239 239 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 370 370 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 627 627 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 662 662 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 740 740 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 804 804 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 835 835 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 848 848 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 859 859 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 884 884 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 915 915 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 998 998 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1004 1004 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1028 1028 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1084 1084 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1096 1096 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1107 1107 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1172 1172 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1188 1188 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1234 1234 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1263 1263 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1330 1330 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1342 1342 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1376 1376 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1444 1444 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1449 1449 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1468 1468 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1535 1535 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1548 1548 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1557 1557 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1643 1643 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1657 1657 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1706 1706 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1730 1730 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1788 1788 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1831 1831 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1863 1863 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1876 1876 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 1987 1987 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2046 2046 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2070 2070 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2121 2121 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2244 2244 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2349 2349 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2391 2391 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2408 2408 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2414 2414 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2563 2563 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2640 2640 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2713 2713 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2749 2749 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2813 2813 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2836 2836 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2873 2873 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2948 2948 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 2986 2986 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 3728 3728 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Glycosylation 3780 3780 . . . Note=N-linked (GlcNAc...) asparagine;Ontology_term=ECO:0000255;evidence=ECO:0000255 O08852 UniProtKB Disulfide bond 436 529 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250 O08852 UniProtKB Disulfide bond 507 521 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250 O08852 UniProtKB Disulfide bond 635 648 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250 O08852 UniProtKB Disulfide bond 642 660 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250 O08852 UniProtKB Sequence conflict 3 3 . . . Note=L->P;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 771 771 . . . Note=R->Q;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 871 871 . . . Note=E->D;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 1180 1180 . . . Note=A->T;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 1292 1292 . . . Note=H->R;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 1632 1632 . . . Note=A->V;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 1684 1684 . . . Note=S->A;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 1770 1770 . . . Note=A->T;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 2085 2085 . . . Note=R->C;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 2507 2507 . . . Note=A->V;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 3956 3956 . . . Note=F->C;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 3962 3962 . . . Note=R->H;Ontology_term=ECO:0000305;evidence=ECO:0000305 O08852 UniProtKB Sequence conflict 4237 4237 . . . Note=Q->R;Ontology_term=ECO:0000305;evidence=ECO:0000305