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A disorder characterized by dental anomalies, gingival overgrowth, and nephrocalcinosis. Dental anomalies include hypoplastic amelogenesis imperfecta, intrapulpal calcifications, delay of tooth eruption, hypodontia/oligodontia, pericoronal radiolucencies and unerupted teeth.




Amelogenesis imperfecta and gingival fibromatosis syndrome
Enamel-renal-gingival syndrome
Enamel-renal syndrome
Hypoplastic amelogenesis imperfecta with nephrocalcinosis


Amelogenesis imperfecta


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