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Definition

A disorder characterized by dental anomalies, gingival overgrowth, and nephrocalcinosis. Dental anomalies include hypoplastic amelogenesis imperfecta, intrapulpal calcifications, delay of tooth eruption, hypodontia/oligodontia, pericoronal radiolucencies and unerupted teeth.

Acronym

AI1G

Synonyms

AIGFS
Amelogenesis imperfecta and gingival fibromatosis syndrome
Enamel-renal-gingival syndrome
Enamel-renal syndrome
ERS
Hypoplastic amelogenesis imperfecta with nephrocalcinosis

Keywords

Amelogenesis imperfecta